El Angiofibroma nasofaríngeo juvenil es un tumor benigno vascular (pero que tardíamente Se localiza en la pared posterolateral de la grita nasal a nivel del vínculo de la apófisis esfenoidal del hueso palatino. Esta localización conforma el. Nasal cavity, paranasal sinuses, nasopharynx – Nasopharyngeal angiofibroma. Juvenile nasopharyngeal angiofibroma (JNA) is a rare and benign but locally in the nasopharynx and nasal cavity, leading to manifestations such as nasal.

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Introduction Although it is a rare neoplasm, accounting for less than 0. Int J Pediatr Otorhinolaryngol. Classification of Fisch Type I: Endoscopic treatment of lesions of the skull base is a branch of surgery that is currently undergoing rapid progress. Based on the Snyderman classification, 3 residual vascularity following preoperative embolization was present in all cases included the sample. Immediate complications of surgery occurred in two patients. Studies comparing surgical treatment with or without embolization have shown that preoperative embolization reduced intraoperative blood loss and the need for replacement of blood products 31, This approach is consistent with the current literature, which recommends that a complete resection through the route associated with the kuvenil morbidity should be attempted whenever possible.

This may have been due to their relatively early diagnosis, when tumors are found smaller and easier to remove completely, as well as due to the use of endoscopic surgery, which assists in controlling tumor removal, including more accurate examinations of the spaces previously occupied by the tumor. Endoscopic Laser-assisted excision of juvenile nasopharyngeal angiofibromas.

For treatment of small lesions, external surgical approaches are gradually being replaced by endoscopic surgery, which can also be combined with conventional angiofibgoma in cases of more advanced disease.


Nasopharyngeal angiofibroma

Arterial embolization in the management of posterior epistaxis. Of our 20 patients, 3 required a combination of endoscopic and open surgery, angiifibroma one, with a Fisch IIIA tumor, having expanded Caldwell-Luc and endoscopic techniques; one, with a Fisch IIIA tumor, undergoing mid-facial degloving and endoscopic surgery; and one, with a Fisch IVA tumor, having mid-facial degloving, craniotomy, and endoscopic surgery Figure 4. Olfactory neuroblastoma Olfactory neuroblastoma.

IIb Full occupation of the pterygomaxillary fossa, anterior displacement of the posterior wall of the maxillary antrum. This makes it possible to precisely stage JNA. The demographic profile, surgical techniques used, immediate and delayed complications, and recurrence rate of the sample are listed in Table 1.

This may be attributed to a rich vasculature and lack of encapsulation. Provisional diagnosis of nasopharyngeal angiofibroma, soft tissue tumor, nasopharyngeal polyp or vascular tumor was made.

Endoscopic approach is an excellent tool in primary and recurrent JNA, it allows visualisation and precise removal of the lesion. Limited juveinl the nasopharynx and nasal cavity.

Angiofibroma nasofaríngeo juvenil – Wikipedia, la enciclopedia libre

Maurice M, Milad M. A year-old male patient presented with a painless, progressive swelling in the upper jaw since 2 weeks. In this study, one patient developed a postoperative decline in visual acuity which remained at the month follow-up, most likely due to inadvertent optic nerve injury during the procedure.

Extended osteoplastic maxillotomy for total excision of giant multicompartmental juvenile nasopharyngeal angiofibroma. This tumor originates in the lateral wall of the nasal cavity, close to the superior border of the sphenopalatine foramen. Treatment for Nasopharyngeal angiofibroma JNA is primarily surgical. Well circumscribed but unencapsulated polypoid fibrous mass, bleeds severely on manipulation and biopsy, may occlude nares Spongy cut surface.

On examination, it may be seen as a pale reddish-blue mass. Views Read Edit View history. There is marked contrast enhancement following administration of contrast, reflecting the prominent vascularity.


Steroid hormone receptor expression in nasopharyngeal angiofibromas. A case report of JNA with rare intra-oral manifestation in a year-old male patient is presented in the article.

Use of neuronavigation techniques, intraoperative MRI, customized instruments, and ever-increasing surgical experience are all factors contributing to further advancements in this field, toward safer and more effective endoscopic approaches. The disease-free period ranged from 10 to 36 months postoperatively.

Juvenile nasopharyngeal angiofibroma

A new endoscopic staging system for angiofibromas. The recurrence rate of endoscopically resected tumors has been shown to be low, and we found that none of our 20 patients experienced tumor recurrence. Received Jul 15; Accepted Jun 1. Although it is a rare neoplasm, juvenile nasopharyngeal angiofibroma JNA is associated with high rates of morbidity and mortality, with the potential for intracranial extension.

Case 3 Case 3. Thank you for updating your details. Intraoperative endoscopy may thus render many osteotomies and bone resections unnecessary, which can decrease the risk of changes in facial growth. Douglas R, Wormald PJ. Log in Sign up. Tumor volume was not associated with bleeding in patients with and without clamping.

They develop at a slightly older age and occur more commonly in women.

Skull base erosion, orbit, infratemporal fossa; residual vascularity. Health care resources for this disease Expert centres Diagnostic tests 1 Patient organisations 24 Orphan drug s 1.

This website is intended for pathologists jucenil laboratory personnel, who understand that medical information is imperfect and must be interpreted using reasonable medical judgment.

We analyzed findings in 20 patients who underwent surgery between and Surgical excision is the main treatment. About Blog Go ad-free.